Right Aortic Arches

Type I Mirror image right arch—will have congenital heart disease 98% of time

• Due to interruption of the left arch just distal to Ductus Arteriosis

• There will be NO posterior impression on the trachea or the barium-filled esophagus

• Descending aorta will be on the right

Type II Right aortic arch with anomalous left subclavian (retroesophageal and retrotracheal) —
associated with cardiac defects 5-10% of the time

• Tetralogy of Fallot most often (71%)

• ASD or VSD next most often (21%)

• Coarctation of the Aorta rarely (7%)

• Due to interruption of the left aortic arch between the LCC and the LSC arteries

• There will be a posterior impression on the trachea and the barium-filled esophagus

• Descending aorta will be on right

Statistics on Mirror Image Right Arches:

If the person has a right arch, then:

* • 90% of the time the congenital heart lesion will be Tetralogy of Fallot

• 6% of the time the congenital heart lesion will be Truncus Arteriosis

• 5% of the time the congenital heart lesion will be Tricuspid atresia

If the person has these heart lesions, they have this chance of also having
a Right Aortic Arch:

* •Truncus arteriosis 33%

•Tetralogy of Fallot 25%

•Transposition 10%

•Tricuspid atresia 5%

•VSD 2%

*apparent discrepancy here due to much higher incidence of TOF than Truncus

WH/